Table 1.
Patient demographics and sJIA disease characteristic
| Study Cohort n=25 (%) |
CARRA Registry Cohort n=389 (%)** |
P Value |
|
|---|---|---|---|
| Age at sJIA diagnosis Mean ± SD (range) |
7.4 ± 5.5 (1.1 – 17.2) | 5.8 ± 4.3 (0.2 – 15.9) | NS* |
| Disease duration (Months) | 51.6 ± 48.8 (8–173)# | 61.9 ± 51 (0.6–219.5) | 0.012 |
| Female | 19 (76) | 213 (55) | 0.040 |
| Race | NS | ||
| Caucasian | 17 (68) | 302 (78) | |
| Black | 7 (28) | 45 (12) | |
| Asian | 1 (4) | 20 (5) | |
| Other/Unknown | 0 (0) | 20 (5) | |
| Ethnicity | NS | ||
| Hispanic | 5 (20) | 50 (13) | |
| Non-Hispanic | 20 (80) | 337 (87) | |
| JIA Symptoms (ever during disease course) | |||
| Fever | 25 (100) | 352 (93) | NS |
| Rash | 23 (92) | 326 (87) | NS |
| Arthritis | 25 (100) | 378 (100) | NS |
| Lymphadenopathy | 19 (76) | 157 (46) | <0.001 |
| Hepato/Splenomegaly | 20 (80) | 102 (31) | <0.001 |
| Serositis | 14 (56) | Unknown | NA |
| Decade of disease onset | 0.0068 | ||
| 1980s | 1 (4) | 0 | |
| 1990s | 5 (20) | 35 (9) | |
| 2000 and later | 19 (76) | 335 (87) | |
| Unknown | 0 | 16 (4) |
*
NS: not significant means P>0.05
**
The sum of all frequencies may not be equal to total sample size due to missing values.
#
At the time of pulmonary diagnosis
NA: Not applicable