Table 3.
Nerve conduction studies and skin biopsies (IENFD) (n = 8).
| Age/Sex | 57/F | 35/F | 30/F | 59/F | 32/M | 26/F | 33/F | 55/M |
| Dorsum Foot | NA | NA | 0 | 0 | 0 | 0 | 0 | NA |
| Distal Leg | NA | NA | 0 | 0 | 0 | 0 | 0 | 0 |
| Thigh | NA | NA | 249 | 88 | 45 | 17 | 15 | 12 |
| IENFD Rank | NA | NA | 3 | 4 | 5 | 6 | 7 | 8 |
| Motor CMAPS (mv) | Med (7.8), F (2.4), T (0.3) | Med (12.6), F (0.1), T(0.3) | Med (6.8), Absent (F/T) | Med (5.5), Absent (F/T) | Med (4.6), Absent (F/T) | Med (3.5), Absent (F/T) | Med (0.1), Absent (F/T) | Absent (Med/F) |
| Sensory NCS (μv) | Med (17.1), R (25.2), S (2.9), Absent (SF) | Med (2.4), R (6.4), Absent (S/SF) | R (3.8), Absent (Med/S/SF) | Absent (Med/R/S/SF) | Absent (Med/R/S/SF) | Absent (Med/R/S/SF) | Absent (Med/R/S/SF) | Absent (Med/R/S/SF) |
| Motor CV (m/s) | Med-APB (58.3), P-EDB (49) | Med-APB (50) | Med-APB (49.4) | Med-APB (48.8) | Med-APB (41.7) | Med-APB (30.1) | NA | NA |
| NCS Rank | 1 | 2 | 3 | 4 | 5 | 6 | 7 | 8 |
| CMTES | 2 | 7 | 7 | 16 | 16 | 12 | 16 | 23 |
APB, abductor pollicis brevis muscle; EDB, extensor digitorum brevis muscle; F, female; IENFD, intraepidermal nerve fiber density, M, male; median, median nerve; NA, not applicable; NCS, nerve conduction studies; F, fibular nerve; R, radial nerve; S, sural nerve; SF, superficial fibular nerve; T, tibial nerve.