Figure 2.
Col4a1 mutation causes small vessel disease, hemorrhagic stroke and macro-angiopathy. (A) Col4a1+/Δex41 mice have porencephaly (penetrance: 80%) and intracerebral hemorrhages (penetrance: 100%) quantified using Prussian blue staining of serial coronal brain sections (scale bar: 1 mm). Data are reported as mean ± standard deviation. (B) Macro-angiopathy with vessel wall thickening, fibrosis and thrombosis advanced with age. Trichrome staining shows collagen deposition (blue) and fibrin accumulation (red) in affected blood vessels (scale bar: 100 μm). No Col4a1+/+ mice had porencephaly, intracerebral hemorrhage or macro-angiopathy (n=32).