Table 1. Clinical details of the patients.
Patient No/Gender/Age (yr) | Corrected Visual Acuity(LogMAR): Right/Left | Horizontal Alignment | MRI (Orbit) | MRI (Cistern Segment) |
---|---|---|---|---|
1/F/24 | 0.2/0.3 | XT | hypoplasia of SR, LPS, IR bilaterally; left MR | Hypoplasia of CNIII bilaterally |
2/M/26 | 0.4/0.3 | XT | hypoplasia of SR, LPS, MR, IR bilaterally | Hypoplasia of CNIII bilaterally, absence of left CNVI |
3/F/18 | 0.2/0.09 | XT | hypoplasia of SR, LPS, MR, IR bilaterally; left LR | Hypoplasia of CNIII bilaterally |
4/F/22 | 0.3/0.2 | XT | hypoplasia of SR, LPS, MR, IR, LR bilaterally | Hypoplasia of CNIII bilaterally, absence of left CNVI |
5/F/23 | 0.4/0.5 | XT | hypoplasia of SR, LPS, MR, IR, LR bilaterally | Hypoplasia of CNIII bilaterally, absence of CNVI bilaterally |
6/F/15 | 0.25/0.2 | XT | hypoplasia of SR, LPS, MR, IR, LR bilaterally | Hypoplasia of CNIII bilaterally |
7/F/18 | 0.2/0.2 | Orthotropic | hypoplasia of SR, LPS, MR, IR bilaterally | Hypoplasia of CNIII bilaterally, absence of right CNVI |
8/F/49 | 0.3/0.48 | XT | hypoplasia of SR, LPS, MR, IR bilaterally | Hypoplasia of CNIII bilaterally, absence of right CNVI |
9/F/24 | 0.4/0.2 | XT | hypoplasia of SR, LPS, MR, IR bilaterally | Hypoplasia of CNIII bilaterally, absence of CNVI bilaterally |
XT, exotropia; SR, superior rectus; IR, inferior rectus; MR, medial rectus; LR, lateral rectus; LPS, levator palpabrae superioris; CNIII, Oculomotor nerve; CNVI, Abducens nerve. All patients had bilateral blepharoptosis, limited supraduction, and essentially complete ophthalmoplegia.