Table I.
Prevalence of Renal Anomalies in Other Alagille Syndrome Series
| Study | Renal Anomaly (Percentage) | Renal Patient Frequency |
|---|---|---|
| Alagille et al 1987 | 73.9% | 17/23 |
| Hoffenberg et al 1995 | 19% | 5/26 |
| Emerick et al 1999 | 40% | 28/69 |
| Quiros –Tejeira et al 1999 | 50% | 15/30 |
| Current study | 39% | 73/187 |