Table II.

Distribution of Renal Anomalies in Alagille Syndrome Study Cohort

Categories of Renal Anomalies	Number of Patients w/ Each Renal Anomaly
Dysplasia	43 (58.9%)
Generalized	28
Focal	8
with Vesicoureteric Reflux	5
with Renal Insufficiency	2
Renal Tubular Acidosis	7 (9.5%)
Vesicoureteric Reflux	6 (8.2%)
with Hydronephrosis	1
Obstruction	6 (8.2%)
Uretero-Pelvic Junction	2
with Hydronephrosis	4
Chronic Renal Failure	4 (5.4%)
Endstage Renal Disease	3 (4.1%)
requiring Kidney Transplant	1
Acute Kidney Injury	2 (2.7%)
Renal Lipidosis	2 (2.7%)
Renal Artery Stenosis (bilateral)	2 (2.7%)
Focal Segmental Glomerulosclerosis	2 (2.7%)
Duplex collecting system	2 (2.7%)
Other	3 (4.1%)