. Author manuscript; available in PMC: 2016 May 1.

Published in final edited form as: J Inherit Metab Dis. 2014 Sep 16;38(3):505–509. doi: 10.1007/s10545-014-9766-8

Table 1.

GSD in Cats and Dogs

Disorder	Enzyme Defect	Breed	Tissue Involvement
Carbohydrates
Type I; von Gierke	Glucose-6-phosphatase	Maltese terrier	Liver, kidney
Type II; Pompe	Acid α-glucosidase	Lapphund dog	Heart, skeletal muscle
Type IIIa; Cori	Glycogen debranching	Curly-coated retriever	Liver, skeletal muscle
Type IV; Andersen	Glycogen branching	Norwegian forest cat	Skeletal muscle, neurons
Type VII; Tarui	Phosphofructokinase	English Springer spaniel	Erythrocytes, skeletal muscle