Table 1.
Case demographicsa and clinical details
Control | All ALS | ALS Subtype | |||
---|---|---|---|---|---|
Presenting deficit | - | - | Upper limb | Lower limb | Bulbar |
N | 5 | 34 | 11 | 14 | 9 |
M:F | 3:2 | 21:13 | 6:5 | 11:3 | 4:5 |
Mean age at death, y (SD) | 67 (10) | 64 (8) | 65 (10) | 62 (9) | 66 (7) |
Range, y | 55-80 | 47-81 | 47-81 | 53-77 | 57-78 |
Mean duration, y (SD) | - | 2 (2) | 3 (2) | 2 (1) | 3 (2) |
Range, y | - | 0.4-7 | 1-3.6 | 0.4-6.1 | 0.6-4.5 |
Mean PMI, h (SD) | 22 (13) | 21 (19) | 18 (18) | 19 (7) | 26 (29) |
Range, h | 12-43 | 5-99 | 5-72 | 7-31 | 5-99 |
aNo differences between groups