Table 3. Studies on the prevalence of systemic autoimmune diseases in PBC patients.
| Author (year) | Country | PBC (n) | SS n (%) | RA n (%) | SLE n (%) | SSc n (%) | PM n (%) | UCTD n (%) |
| Marasini et al (2001) 57 | Italy | 170 | 6 (3.5%) | 3 (2) | 3 (2) | 21 (12) | 1 (1) | 12 (7) |
| Gershwin et al (2005) 58 | USA | 1032 | 102 (10) | 103 (10) | 27 (3) | 24 (2) | 6 (0.6) | - |
| Wang et al (2013) 59 | China | 322 | 121 (36) | 9 (2.8) | 12 (4%) | 9 (3) | 10 (3) | - |
| TOTAL | 1524 | 229 (15) | 112 (7.5) | 42 (3) | 53 (3.5) | 17 (1) | 12 (0.8) |
PBC, primary biliary cirrhosis; PM, polymyositis; RA, rheumatoid arthritis; SLE, systemic lupus erythematosus; SS, Sjögren syndrome; SSc, systemic sclerosis; UCTD, undifferentiated connective tissue disease