Table 2. Summary of clinical data of affected individuals of family JX-H016.

Patient	Gender	Age (years)		Use of aminoglycoside	Hearing test PTAa (dB)		Audiogram shape	Tinnitus	Vertigo	Noise exposure
		At testing	At onset		Left ear	Right ear
III-1	Female	—	Prelingual	—	—	—	—	—	—	—
III-2	Female	36	Prelingual	No	—	—	—	—	—	—
III-4	Female	35	Prelingual	No	97	100	Flat	No	No	No
III-10	Male	—	Prelingual	—	—	—	—	—	—	—
III-11	Female	35	Prelingual	No	100	90	Sloping	No	No	No
III-13	Female	27	Prelingual	No	98	98	Flat	No	No	No
III-15	Female	24	Prelingual	No	100	100	Flat	No	No	No
III-17	Male	29	Prelingual	No	88	90	Flat	No	No	No
III-20	Female	—	Prelingual	Yes	—	—	—	—	—	—
III-22	Female	—	Prelingual	Yes	—	—	—	—	—	—
III-24	Female	28	Prelingual	Yes	82	83	Sloping	No	No	No
III-29	Male	17	Prelingual	Yes	77	82	Sloping	No	No	No

^aPTA, pure-tone average.