Table 2.
Psychopathological and neuropsychological results of DM1, FSHD and control subjects
| Characteristics | DM1 | FSHD | Controls |
|---|---|---|---|
| N | 38 | 19 | 20 |
| Psychopathology | |||
| Apathy, % | 39.5 | 21.1 | 0 |
| LARS, mean (SD) | −16.9 (8,5)ba | −22.8 (6.3) | −25.4 (4.8) |
| LARS-IC, mean (SD) | −1.53 (1.2)ba | −2.45 (.7) | −2.7 (.7) |
| LARS-E, mean (SD) | −2.1 (1.4)a | −2.66 (1.2) | −2.9 (1.2) |
| LARS-AI, mean (SD) | −2.44 (1.1)a | −2.73 (1.1) | −3.05 (.7) |
| LARS-SA, mean (SD) | −1.79 (2.1)a | −2.3 (1.6) | −2.21 (1.7) |
| MADRS, mean (SD) | 10.3 (8.8) | 7.0 (7.4) | 6.1 (6.2) |
| STAI-A, T score, mean (SD) | 50.1 (14.1) | 44.8 (11) | 45.3 (9) |
| STAI-B, T score, mean (SD) | 53.3 (12.6) | 48.7 (12.9) | 47.1 (10.9) |
| KFSS, mean (SD) | 4.6 (1.5)a | 4.8 (1.5)c | 3.3 (1.0) |
| Neuropsychology | |||
| MMSE, mean (SD) | 27.5 (2.2)ba | 28.9 (0.9) | 29.3 (0.9) |
| FAB, mean (SD) | 15.5 (1.7)a | 15.9 (1.4) | 16.5 (0.95) |
| Stroop word T score, mean (SD) | 47.8 (6.6) | 51.6 (8.9) | 51.8 (7) |
| Stroop color T score, mean (SD) | 44.24 (8.2) | 46.56 (9.8) | 49.75 (6.3) |
| Stroop color-word T score, mean (SD) | 39.0 (9.9)ba | 49.2 (7.9) | 51.8 (4.9) |
| Stroop interference score, mean (SD) | 44.47 (8.4)ba | 49.68 (6.5) | 50.65 (6.6) |
| TMT-A z score, mean (SD) | 0.2 (0.7)ba | 0.9 (0.4) | 1.0 (0.5) |
| TMT-B z score, mean (SD) | −0.4 (1.2)ba | 0.4 (0.6) | 0.4 (0.7) |
LARS-IC LARS Intellectual curiosity, LARS-E LARS Emotion, LARS-AI LARS Action initiation, LARS-SA LARS Self-awareness, MADRS Montgomery Asberg Depression Rating Scale, STAI-A state anxiety, STAI-B trait anxiety, KFSS Krupp fatigue severity scale, MMSE Mini Mental State Evaluation, FAB Frontal Assessment Battery, TMT Trail Making Test
aSignificant difference between DM1 and Controls, p < 0.05
bSignificant difference between DM1 and FSHD, p < 0.05
cSignificant difference between FSHD and Controls, p < 0.05