Table 1.
Summary of 15 consecutive patients with ectopia lentis
| Case no/sex/age at initial visit/final visit (years) | Visible equator of the lens in both eyes | Family history of ectopia lentis | Diagnosis | Age at surgery | The reason for surgery | Visual acuitya & refractive error (diopter) at distance RE LE |
Visual acuitya at near RE LE |
Visual acuityb & refractive error (diopter) at distance after surgery RE LE |
|---|---|---|---|---|---|---|---|---|
| 1/M/3/16 | Temporal | Grandfather (aphakia) Mother (Case 3) Sister (Case 2) |
Familial ectopia lentis | 16 IOL suture in both eyes |
Difficulty in school class | 0.07 s.-2.0 c.-2.0A180 | 0.6 | 0.6 s.+2.5 c.-5.0A10 |
| 0.06 s.-2.0 c.-2.5A180 | 0.6 | 0.6 s.+0.75 c.-3.5A25 | ||||||
| 2/F/7/13 | Temporal | Grandfather (aphakia) Mother (Case 3) Brother (Case 1) |
Familial ectopia lentis | Not done | 0.1 s.+2.0 c.-4.0A90 | 0.4 | ||
| 0.1 s.+2.0 c.-4.0A90 | 0.4 | |||||||
| 3/F/36/42 | Temporal | Father (aphakia) Son (Case 1) Daughter (Case 2) |
Familial ectopia lentis | 36 IOL suture in both eyes |
Cataract in both eyes | 0.1 s.-16.0 c.-1.0A180 | 0.1 | 1.0 s.-2.5 c.-0.5A125 |
| 0.1 s.-16.0 c.-1.0A180 | 0.1 | 0.9 s.-0.75 c.-1.0A180 | ||||||
| 4/M/2/10 | Nasal | Father (aphakia) Brother (Case 5) Sister (Case 6) |
Marfan syndrome | Not done | 1.0 s.-10.0 c.-2.0A180 | 0.9 | ||
| 0.4 s.-10.0 c.-3.0A10 | 0.3 | |||||||
| 5/M/5/14 | Nasal | Father (aphakia) Brother (Case 4) Sister (Case 6) |
Marfan syndrome Funnel chest |
12 | Aphakic optical axis in RE | 0.04 s.+14.5 c.-0.75A180 | 0.1 | 0.9 s.+15.0 c.-1.0A180 |
| 0.8 s.-13.5 c.-3.0A20 | 0.6 | 1.5 s.+14.0 c.-1.5A180 | ||||||
| 6/F/9/17 | Nasal | Father (aphakia) Brother (Case 4) Brother (Case 5) |
Marfan syndrome Mitral valve prolapse |
Not done | 0.9 s.-8.5 c.-2.0A180 | 0.9 | ||
| 1.0 s.-8.5 c.-2.0A180 | 0.9 | |||||||
| 7/M/6/15 | Inferonasal | None | Marfan syndrome Scoliosis |
Not done | 0.9 s.-1.5 | 0.4 | ||
| 0.4 s.-1.25 c.-3.0A180 | 0.1 | |||||||
| 8/F/2/8 | Inferonasal | None | Marfan syndrome Mitral valve prolapse Scoliosis |
Not done | 0.5 s.-12.25 | 0.2 | ||
| 0.3 s.-12.25 | 0.4 | |||||||
| 9/M/3/8 | Temporal | None | Sporadic ectopia lentis | 6 | Traumatic lens dislocation to anterior chamber in RE | 0.5 s.-8.0 | 0.5 | 1.0 s.+15.75 c.-2.0A180 |
| 0.3 s.-8.0 | 0.3 | 1.0 s.+15.25 c.-1.25A180 | ||||||
| 10/M/3/7 | Inferior | Mother (aphakia) Brother (Case 11) |
Familial ectopia lentis | Not done | 0.8 s.-3.0 c.-6.0A10 | 0.9 | ||
| 1.0 s.-0.5 c.-5.5A180 | 0.9 | |||||||
| 11/M/2/4 | Inferior | Mother (aphakia) Brother (Case 10) |
Familial ectopia lentis | Not done | 0.3 s.-4.5 c.-2.25A25 | 0.4 | ||
| 0.2 s.-7.0 c.-5.0A13 | 0.4 | |||||||
| 12/F/5/9 | Inferonasal | Father | Marfan syndrome | 6 | Difficulty in school class | 0.2 s.-5.5 c.-5.0A50 | 0.3 | 1.2 s.+14.0 c.-1.0A180 |
| 0.1 s.0 c.-4.0A180 | 0.1 | 1.5 s.+14.0 c.-1.5A180 | ||||||
| 13/M/4/7 | Temporal | None | Sporadic ectopia lentis | 4 | Aphakic optical axis in RE | 0.07 s-4.5 c.-2.75A165 | 0.2 | 1.0 s.+15.0 c.-1.0A20 |
| 0.06 s.-7.0 c.-5.0A13 | 0.2 | 1.0 s.+15.0 c.-1.0A150 | ||||||
| 14/M/5/9 | Inferonasal | Mother Grandmother |
Familial ectopia lentis Moderate mental retardation Autism |
Not done | 0.1 s.-6.0 | 0.4 | ||
| 0.1 s.-6.0 | 0.4 | |||||||
| 15/F/6/6 | Inferior | None | Sporadic ectopia lentis | Not done | 0.8 s.-0.5 c.-2.5A170 | 0.9 | ||
| 0.8 s.-1.0 c.-5.25A175 | 0.8 |
RE right eye, IOL intraocular lens, s. spherical, c. cylindrical, A axis
aVisual acuity: best-corrected visual acuity at the final visit in patients with observation while best-corrected visual acuity just before the surgery in patients with lensectomy. Refractive error, determined basically by autorefraction and also by trial-lens exchange in elder patients
bVisual acuity: best-corrected visual acuity at the final visit