Table 3. Htt-polyQ aggregate-associated proteins found in inclusions and aggregates in various neurodegenerative diseases.

Gene/Protein Name	Disease or Disease Model	ID Domain	RBP	PQC	Reference
AAK1	ALS-SOD1	209, 81, 50			[100]
FUS	ALS	284, 71, 87	yes		[101–103]
HNRNPA3	ALS	39	yes		[104]
HSPA8	HD & SCA1	46, 36		yes	[94, 105]
MATR3	ALS	31, 57, 42, 119, 72	yes		[106]
MLF2	HD	136			[107]
NONO	ALS-FUS	66	yes		[108]
PPIA	ALS-SOD1	None	yes	yes	[109]
RAD23B	HD, SCA3	120, 67, 41		yes	[110, 111]
SQSTM1	PD & ALS	153		yes	[112–115]
SUCLG2	AD	None			[116]
SUMO2	HD & ALS	None		yes	[117, 118]
TARBP (TDP-43)	ALS	45, 55	yes		[119, 120]
TCERG1	HD	138, 177, 70, 36	yes		[74]
TCF20	HD	87, 739, 50, 32, 709, 34, 121	yes		[121]
TFG	CMTD	35, 54, 105			[122]
TGM3	HD	49			[123]
UBQLN2	ALS	62, 58, 42, 81, 31, 84		yes	[124]
YWHAB	ALS	None			[125]

The numbers for ID Domains indicate the length of distinct unstructured regions ≥30, for the identified rat proteins from PC-12 cells, as determined by IUPred-L. RBP = RNA-binding protein as described in the legend of Table 2; PQC = protein quality control.