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. 2015 Sep 1;13(1):19. doi: 10.1186/s12948-015-0025-9

Table 1.

Summary of reported case records and retrospective/prospective studies

References Main organ involvement Dose Outcome
Gottenberg et al. [17] Lymph nodes 4 × 375 mg/m2 Good
Belkhou et al. [15] Lymph nodes 2 × 1 g, every 2 weeks Good
Dasilva et al. [13] Lymph nodes, including peritoneal Two infusions, dose not specified Good
Bomprezzi et al. [11] CNS and skin 2 × 1 g, every 2 weeks, then 1 g every 6 months for 2 years Good
Lower et al. [14] Eye; 2 of 4 patients also had significant lung involvement 2 × 1 g, every 2 weeks, then 375 mg/m2 every 4 or 8 weeks for a minimum of 24 months or 1 g every 4 weeks for 10 months Three responders of four patients
Sawaya et al. [12] Neuromyelitis optica and lymph nodes Single 1 g infusion Good
Sweiss et al. [16] Lung 2 × 1 g, every 2 weeks Seven full or partial responders of ten patients