(A) Quantitation of granulopoietic
differentiation of myeloid progenitors derived from SCN iPSCs (SCN15) in
liquid culture containing G-CSF at 50 ng/ml, 1,000 ng/ml, and 50 ng/ml,
along with 230 nM sivelestat (a small-molecule inhibitor of NE).
(B) Wright-Giemsa–stained cytospin at the end of the
culture in A. (C) Quantitation of granulopoietic
differentiation of myeloid progenitors derived from SCN iPSCs (SCN14) in
liquid culture containing G-CSF at 50 ng/ml, 1,000 ng/ml, and 50 ng/ml,
along with 230 nM sivelestat. (D) Wright-Giemsa–stained
cytospin at the end of the culture in C. (E and
F) qPCR analyses of the mRNA for CEBPB
(E) and CEBPA (F) in
promyelocytes derived from control or ELANE-mutant SCN
iPSCs. In A and C, data from 4 independent
experiments are plotted as mean ± SD. In E and F,
individual data from 2 or more independent experiments with duplicates are
plotted as mean ± SD. Scale bars: 10 μm. Cont,
control.