Table 1.
Cases | Gender | Age (years) | Grade (0–4) | CAGn Repeats | CAGn Repeats |
---|---|---|---|---|---|
Huntington’s disease | |||||
HD1 | M | 71 | 1 | 19 | 46 |
HD2 | M | 61 | 2 | 17 | 46 |
HD3 | F | 78 | 2 | 17 | 43 |
HD4 | M | 57 | 3 | 19 | 47 |
HD5 | F | 64 | 4 | 19 | 45 |
HD6 | M | 60 | 1 | 23 | 46 |
HD7 | M | 71 | 1 | 17 | 44 |
HD8 | F | 61 | 2 | 19 | 46 |
HD9 | M | 66 | 3 | 17 | 45 |
HD10 | M | 77 | 3 | 24 | 43 |
HD11 | M | 77 | 3 | 19 | 43 |
HD12 | M | 73 | 3 | 21 | 45 |
HD13 | M | 68 | 4 | 19 | 45 |
HD14 | M | 58 | 4 | 20 | 48 |
HD15 | M | 40 | 4 | 18 | 51 |
HD16 | F | 26 | 4 | 22 | 70 |
F:M 4:12 | Average 63 ± 13.80 | ||||
Sporadic tauopathies | |||||
AD | F | 78 | 18 | 18 | |
PSP | M | 75 | 20 | 20 | |
PiD | F | 68 | 19 | 24 | |
CBD | M | 79 | 28 | 33 | |
F:M 2:2 | Average 75 ± 4.97 | ||||
Controls | |||||
CTL1 | M | 67 | 0 | 20 | |
CTL2 | M | 72 | 0 | 21 | |
CTL3 | M | 69 | 0 | 20 | |
CTL4 | M | 80 | 0 | 20 | |
CTL5 | F | 83 | 0 | 19 | |
F:M 1:4 | Average 74.2 ± 6.98 |
AD = Alzheimer's disease; CBD = corticobasal degeneration; PiD = Pick's disease; PSP = progressive supranuclear palsy.