Table 1. Clinical characteristics of DBA patients (*patient in clinical remission; **two analysis performed in two independent samples; ^┼three different analysis a few years apart; ^▲two different analysis a few years apart).

The ranges of PB BFU-E BASAL and BM BFU-E BASAL of healthy individuals are 16.0+/-8.0 and 57.0+/-28, respectively. The normal range of e-ADA is 0,8–1,2 U/g Hb.

DBA PATIENTS	SEX	AGE	AGE AT ONSET	TREATMENT	Hb (g/dL)	MCV (fL)	RBC (10^6/uL)	Reticulocytes (10^9/L)	eADA (U/g Hb)	BM	BM BFU-E BASAL	BM BFU-E WITH SCF	PB BFU-E BASAL	PB BFU-E WITH SCF
1	M	24	2 months	TRANSFUSION	8.0	88.8	3.04	13.5	3.2	ERYTHROID APLASIA	0	46	0	1
2	F	43	At birth	STEROIDS	10.7	89.8	3.54	N/D	3.9	ERYTHROID HYPOPLASIA	N/D	N/D	1	7
3	M	7	1 month	TRANSFUSION	6.8; 6.8**	80.9; 70.8**	2.34; 2.39**	2.8; 5.1**	N/D	ERYTHROID HYPOPLASIA	23	26	1	8
4	M	5	1 year	TRANSFUSION	9.5	79.8	3.20	10.7	N/D	ERYTHROID APLASIA	0	0	N/D	N/D
5	F	27	2 months	NONE*	10.9	83.8	3.78	45.8	5.3	ERYTHROID APLASIA	0	7	N/D	N/D
6	F	4	At birth	TRANSFUSION	9.6	82.1	3.36	6	N/D	ERYTHROID APLASIA	0; 5; 20┼	2; 74; 46┼	0; 0▲	0; 2▲
7	M	37	1 year	NONE*	11.7	106.8	3.27	35.7	4.1	ERYTHROID HYPOPLASIA	7	41	N/D	N/D
8	F	5	6 months	TRANSFUSION	6.2	81.8	2.12	11.6	2	N/D	N/D	N/D	N/D	N/D
9	F	17	3 months	STEROIDS	11.5	99.6	3.30	42.8	2.6	ERYTHROID APLASIA	0; 5▲	62; 54▲	N/D	N/D
10	M	13	2 months	STEROIDS	12.6	91.4	4.06	105.0	3.4	ERYTHROID APLASIA	12	89	N/D	N/D
11	M	12	2 months	TRANSFUSION	9.0	81.9	3.20	17.7	N/D	NORMAL	N/D	N/D	N/D	N/D
12	M	20	1 year	NONE	15.2	89.7	4.8	62.3	5	ERYTHROID HYPOPLASIA	0; 0▲	2; 52▲	N/D	N/D
13	M	25	4 months	TRANSFUSION	10.1	85.6	3.4	45	N/D	ERYTHROID APLASIA	N/D	N/D	N/D	N/D