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. 2015 Sep 16;7:ecurrents.hd.c63b441d04bb6738c0234f91c2b3e312. [Version 1] doi: 10.1371/currents.hd.c63b441d04bb6738c0234f91c2b3e312

Table 2.

Amino acid concentrations

Plasmaa Urineb
HD patients Controls HD patients Controls
Alanine 256 (235-393) 288 (236-444) 37.0 (21.5-43.2) 28.5 (27.6-39.1)
Arginine 99 (69-107) 102 (71-109) 2.2 (1.5-2.7) 2.0 (1.7-2.9)
Asparagine 42 (34-51) 52 (37-58) 13.6 (8.8-23.2) 14.8 (10.7-16.0)
Aspartic acid 9 (8-13) 11 (11-13) 12.6 (11.3-14.2) 11.6 (10.7-12.5)
Citrulline 38 (32-47) 42 (39-45) 0.5 (0.5-2.0)c 0.5 (0.5-0.8)c
Cystathionine 2 (2-3) 2 (2-3) 2.3 (0.9-2.7)c 1.1 (0.5-2.5)c
Cystine - - 7.1 (5.8-9.7) 5.6 (4.8-6.5)
Glutamine 626 (530-685) 611 (550-692) 59.3 (35.9-84.0) 45.3 (43.0-57.8)
Glutamic acid 40 (32-67) 40 (34-52) 2.9 (2.3-4.0) 2.7 (2.0-3.3)
Glycine 223 (158-282) 256 (209-307) 129.1 (105.2-286.0) 136.1 (118.5-197.7)
Histidine 75 (63-92) 82 (74-88) 78.1 (46.6-139.7) 79.3 (59.0-94.7)
Isoleucine 60 (53-80) 68 (57-82) 1.5 (0.5-1.7)c 1.1 (0.5-1.6)c
Leucine 133 (104-149) 140 (101-164) 2.9 (2.0-4.1) 3.0 (2.2-3.4)
Lysine 183 (141-218) 187 (176-213) 24.6 (20.9-49.0) 23.4 (20.6-30.9)
Methionine 24 (20-32) 24 (22-34) 2.3 (1.7-2.5) 1.8 (1.4-2.4)
Ornithine 47 (42-58) 47 (39-59) 2.6 (1.3-3.1) 3.0 (1.7-3.9)
Phenylalanine 62 (51-76) 61 (53-73) 6.8 (5.3-8.7) 5.6 (4.1-6.7)
Proline 191 (154-247) 190 (168-264) ND ND
Serine 105 (77-125) 111 (107-122) 43.8 (24.0-65.0) 41.4 (35.9-44.6)
Taurine 33 (29-43) 34 (32-43) 84.2 (33.5-100.7) 64.3 (22.9-95.9)
Threonine 113 (95-161) 123 (113-146) 19.1 (10.9-25.6) 15.9 (11.2-18.1)
Tryptophan 59 (36-72) 56 (50-67) ND ND
Tyrosine 55 (42-64) 55 (49-66) 10.1 (7.3-16.8) 9.8(6.6-12.1)
Valine 246 (202-257) 247 (203-261) 4.4 (3.2-6.9) 3.9 (3.3-5.0)