Table 1. Baseline characteristics of all the patients treated with ANA.
Patient | Gender | Age at baseline (years) | Disease duration at baseline (months) | Family history of ALS | C9orf72 repeats | Exclusive LMND | Disease onset | ALSFRSr at baseline | VC at baseline | VC final |
---|---|---|---|---|---|---|---|---|---|---|
1 | Male | 59 | 36 | No | 1700 | No | LE | 38 | 103 | 98 |
2 | Male | 59 | 25 | No | - | Yes | UE | 42 | 91 | 88 |
3 | Male | 51 | 21 | No | - | Yes | UE | 44 | 83 | 70 |
4 | Male | 52 | 11 | No | - | No | LE | 38 | 58 | 42 |
5 | Male | 51 | 26 | No | - | Yes | LE | 42 | 72 | 49 |
6 | Male | 72 | 15 | No | - | Yes | LE | 46 | 101 | 94 |
7 | Male | 69 | 26 | No | - | No | UE | 43 | 89 | 84 |
8 | Male | 49 | 24 | No | - | Yes | LE | 38 | 104 | 86 |
9 | Male | 60 | 18 | No | 2400 | No | UE | 43 | 82 | 24 |
10 | Male | 59 | 15 | No | 2000 | Yes | UE | 45 | 76 | 52 |
11 | Male | 45 | 36 | No | - | No | LE | 37 | 79 | 66 |
12 | Male | 53 | 18 | No | n.d. | Yes | LE | 38 | 83 | 71 |
13 | Male | 59 | 10 | No | n.d. | Yes | LE | 38 | 86 | 67 |
14 | Male | 66 | 16 | No | - | No | UE | 47 | 85 | 68 |
15 | Female | 60 | 39 | No | 2300 | Yes | LE | 42 | 92 | 111 |
16 | Male | 63 | 27 | No | - | No | UE | 32 | 73 | 47 |
17 | Male | 49 | 18 | No | - | Yes | UE | 39 | 66 | 51 |
Mean (SD) | 57.4 (7.5) | 22.4 (8.6) | 40.7 (3.9) | 83.7 (12.6) | 68.7 (22.9) |