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. 2015 Oct 7;10(10):e0139684. doi: 10.1371/journal.pone.0139684

Table 1. Baseline characteristics of all the patients treated with ANA.

Abbreviations: ALSFRSr = amyotrophic lateral sclerosis functional rating scale–revised. LMND = lower motor neuron disease. VC = respiratory viral capacity. UE = upper extremity. LE = lower extremity. n.d. = not determined.

Patient Gender Age at baseline (years) Disease duration at baseline (months) Family history of ALS C9orf72 repeats Exclusive LMND Disease onset ALSFRSr at baseline VC at baseline VC final
1 Male 59 36 No 1700 No LE 38 103 98
2 Male 59 25 No - Yes UE 42 91 88
3 Male 51 21 No - Yes UE 44 83 70
4 Male 52 11 No - No LE 38 58 42
5 Male 51 26 No - Yes LE 42 72 49
6 Male 72 15 No - Yes LE 46 101 94
7 Male 69 26 No - No UE 43 89 84
8 Male 49 24 No - Yes LE 38 104 86
9 Male 60 18 No 2400 No UE 43 82 24
10 Male 59 15 No 2000 Yes UE 45 76 52
11 Male 45 36 No - No LE 37 79 66
12 Male 53 18 No n.d. Yes LE 38 83 71
13 Male 59 10 No n.d. Yes LE 38 86 67
14 Male 66 16 No - No UE 47 85 68
15 Female 60 39 No 2300 Yes LE 42 92 111
16 Male 63 27 No - No UE 32 73 47
17 Male 49 18 No - Yes UE 39 66 51
Mean (SD) 57.4 (7.5) 22.4 (8.6) 40.7 (3.9) 83.7 (12.6) 68.7 (22.9)