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. 2015 Oct 7;10(10):e0138113. doi: 10.1371/journal.pone.0138113

Table 1. Clinical severity score scale.

Severity Score (SS) 0 1 2 3
Seizures Absent Easily managed with meds Managed with meds but occasional breakthrough Recalcitrant seizures multiple meds
Gait Normal Mildly apraxic Requires support for walking Requires support to stand; wheelchair bound
Scoliosis Absent <20 degree 20–30 degrees >30 degree, requires surgery
Respiratory Irregularity Absent Minimal BH BH and HV > half the wake period BH and HV > half wake period, ± cyanosis
Hand Use Normal Purposeful grasping Tapping for needs No hand use
Speech Normal Sentences/phrases Single words Non-verbal
Sleep Normal Awakens but falls back to sleep Fragmented night sleep with daytime sleepiness Unable to sleep through the night

BH = breath holding; HV = hyperventilation