Table 1. Clinical severity score scale.
Severity Score (SS) | 0 | 1 | 2 | 3 |
---|---|---|---|---|
Seizures | Absent | Easily managed with meds | Managed with meds but occasional breakthrough | Recalcitrant seizures multiple meds |
Gait | Normal | Mildly apraxic | Requires support for walking | Requires support to stand; wheelchair bound |
Scoliosis | Absent | <20 degree | 20–30 degrees | >30 degree, requires surgery |
Respiratory Irregularity | Absent | Minimal BH | BH and HV > half the wake period | BH and HV > half wake period, ± cyanosis |
Hand Use | Normal | Purposeful grasping | Tapping for needs | No hand use |
Speech | Normal | Sentences/phrases | Single words | Non-verbal |
Sleep | Normal | Awakens but falls back to sleep | Fragmented night sleep with daytime sleepiness | Unable to sleep through the night |
BH = breath holding; HV = hyperventilation