Fig. 5.

Glycosaminoglycan (GAG) levels in skin-cultured fibroblasts from patients 5, 6, and 11 (P5, P6, and P11, respectively), and a healthy individual upon gentamicin treatment. Patient fibroblasts affected by a mucopolysaccharidosis and responsive to gentamicin treatment were treated for 72 h with or without 300 μM gentamicin. Total GAG content was assessed and results are shown as μg GAGs per mg of protein (*p < 0.05) and compared with fibroblasts from a healthy individual