Table 1.
ADAMTS13 deficiency in clinical series of “thrombotic thrombocytopenic purpura”
| Authors | Exclusion of renal failure | Exclusion of secondary cases | Severe deficiency |
|---|---|---|---|
| Tsai, et al 4 | Yesa | Yesc | 100% |
| Zhou, et al 5 | Yesa | Yesc | 100% |
| Furlan, et al 6 | Yesb | No | 83% |
| Veyradier, et al 7 | Yesb | Yesd | 89% |
| Hovinga, et al 8 | Yesb | Yesd | 57% |
| Matsumoto, et al 9 | Yesb | Yesd | 52% |
| Coppo, et al 10 | No | Yesd | 67% |
| Terrel, et al 11 | No | Yesd | 34% |
| Peyvandi, et al 12 | No | No | 48% |
| Bohm, et al 13 | Not stated | No | 91% |
| Rick, et al 14 | Not stated | No | 78% |
| Kokame, et al 15 | Not stated | Not stated | 80% |
a
Peak Cr > 3.0 mg/dL.
b
Diagnosis was provided by participating centers using undisclosed criteria.
c
Based on assessment of the entire courses.
d
Based on initial clinical assessment or not specified.