Table 1.
History and baseline lab values.
| PN | FH | NJ | TX Aage | MCHC, g/dL | RDW% | Retic% |
|---|---|---|---|---|---|---|
| 1 | Y | Y | None | 34.6 | 14.1 | 3.8 |
| 2 | Y | Y | 2 m | 35 | 20.3 | 9.5 |
| 3 | N | N | None | 36 | 14.1 | 6 |
| 4 | Y | Y | 76 m | 36 | 25 | 12 |
| 5 | N | Y | 3.5 m | 34.9 | 16.1 | 8.9 |
| 6 | Y | Y | 84 m | 38 | – | 10.6 |
| 7 | Y | Y | 21 d | 36.5 | 23 | 10 |
| 8 | Y | Y | 16 d | 35 | 21.5 | 7 |
| 9 | Y | Y | 17 d | 35.4 | 19.4 | 9.6 |
| 10 | Y | Y | 8 d | 36.2 | 17.8 | 6.5 |
| 11 | Y | Y | 91 m | 35 | 20.4 | 7.7 |
| 12 | Y | Y | None | 36.8 | 17.1 | 4.2 |
| 13 | N | Y | 13 d | 36.7 | 20.8 | 8.7 |
| 14 | Y | Y | 108 m | 36 | 28 | 11.8 |
| 15 | Y | Y | 183 m | 37.5 | 20.5 | 11.5 |
| 16 | Y | Y | 42 m | 34.7 | 28.3 | 13.8 |
| 17 | N | Y | Infant | 35.2 | 18.4 | 8 |
| 18 | N | Y | 21 d | 34.5 | 26 | 12 |
| 19 | Y | Y | NICU | 36.7 | 12.7 | 2.7 |
| 20 | Y | Y | 25 m | 35.5 | 20.4 | 2.4 |
| 21 | N | Y | 160 m | 37.5 | 18.5 | 9 |
| 22 | Y | Y | 114 m | 36.4 | 15.2 | 5.4 |
| 23 | N | Y | NICU | 35.5 | 24.2 | 13.1 |
| 24 | Y | N | None | 35.8 | 14.5 | 2.4 |
| 25 | Y | Y | None | 35.6 | 20.6 | 18.6 |
| 26 | Y | N | None | 36.3 | 18.4 | 12.8 |
| 27 | Y | Y | None | 35.7 | 19 | 3 |
| 28 | Y | Y | 60 m | 36 | 17 | 5 |
| 29 | Y | Y | 47 m | 35.3 | 19 | 7 |
| 30 | Y | Y | None | 37.5 | 16.5 | 4 |
PN: patient number; FH: family history; Y: positive; N: negative; NJ: neonatal jaundice; TX Age: age at first transfusion in days (d) or months (m); MCHC: mean corpuscular hemoglobin concentration; RDW: red cell distribution width.
MCHC mean = 35.9; standard deviation = 0.93; RDW mean = 19.5; standard deviation = 4.0.