Table 1.
Combined anomaly | Clinical symptoms | Preoperative Duplex USG | Embolization of portosystemic shunt | Combined splenectomy | Follow-up (months) | ||||
---|---|---|---|---|---|---|---|---|---|
Patient | Sex/age (yr) | Graft type | Outcome | ||||||
1 | M/20 | - | EV, S, HS | Absent | CV | + | + | 30 | Good evolution |
2a | M/1 | + | EV, S | Present | CV | + | - | 30 | Good evolution |
3 | M/19 | - | EV, S, HS | Absent | CV | + | - | 24 | Good evolution |
4 | M/10 | - | EV, S, HS | Present | IMV | + | - | 23 | Good evolution |
5 | F/4 | + | EV, S, HS | Absent | IMV | - | - | 10 | Good evolution |
6b | M/13 | + | EV, S, HS | Absent | CV | - | + | 10 | Good evolution |
Combined anomalies: Patient 2, dextrocardia and intestinal malrotation; Patients 5, congenital heart disease; Patient 6, imperforate anus
Preoperative Duplex USG: Present, visualization of intrahepatic portal vein; Absent, non-visualization of intrahepatic portal vein
EV esophageal varix bleeding, S splenomegaly, HS hypersplenism, USG ultrasonography, CV coronary vein, IMV inferior mesenteric vein
aPercutaneous transluminal angioplasty at 19 months after meso-Rex bypass
bPast history of distal spleno-renal shunt operation at 58 months before meso-Rex bypass