Table 1.
Etiology | Unknown |
Incidence | Rare; 0.2 – 0.5 cases / million. |
Gender ratio | Predominantly affects males |
Age predilection | Boys and young men |
Risk factors | No known risk factors |
Treatment | Surgical resection, chemotherapy, and radiation |
Prognosis | Poor |
Imaging findings | Multiple, lobular abdominal masses, which can grow very large, typically with a dominant lesion and multifocal peritoneal/omental/retroperitoneal masses, often involving the retrovesical region. |