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. 2015 Aug 27;107(11):djv214. doi: 10.1093/jnci/djv214

Table 5.

Mutation frequency by family history in UCKFOCSS subjects*

Family history Carrier status BARD1 BRIP1 NBN PALB2
No. (%) No. (%) No. (%) No. (%)
1 ovarian cancer, ≤2 breast cancer case (age <60 y) Carrier 1 (33.3) 5 (41.7) 2 (66.7) 4 (57.1)
Noncarrier 1087 (56.4) 1083 (56.4) 1086 (54.3) 1084 (56.3)
2 ovarian cancer Carrier 1 (33.3) 6 (50.0) 0 (0) 1 (14.3)
Noncarrier 558 (28.9) 553 (28.7) 559 (29.0) 559 (29.0)
Other related cancers in extended family Carrier 1 (33.3) 1 (8.3) 1 (33.3) 2 (28.6)
Noncarrier 283 (14.7) 283 (14.7) 283 (14.7) 282 (14.6)

* Thirty individuals with one ovarian cancer and three colorectal cancers (1 age <50 y) in primary relatives and 39 individuals with three or more breast cancers had no carriers detected for any gene. UKFOCSS = United Kingdom Familial Ovarian Cancer Screening Study.