Table 1.
Neuropathology-Confirmed Prion Disease Cases in the National Alzheimer’s Coordinating Center Database With No Mention of a Clinical Diagnosis of Prion Disease in Medical Records, 1984 to 2005.
| Year of Death | Age | Sex | Clinical Diagnosis | Final Diagnosis | Illness Duration | |
|---|---|---|---|---|---|---|
| Case 1 | 1999 | 47 | F | AD | GSS | NA |
| Case 2 | 2000 | 47 | F | Dementia NOS | CJD | 15+ years |
| Case 3 5 | 1994 | 49 | M | AD | fCJD | 8 years |
| Case 4 | 2000 | 72 | M | PSP | CJD | NA |
| Case 5 | 1996 | 78 | F | AD | CJD/AD/Wernicke–Korsakoff syndrome | NA |
| Case 6 | 1995 | 81 | M | AD | GSS; or CJD with concomitant AD | 7 years |
| Case 7 | 2000 | 88 | M | AD | CJD/AD | NA |
Abbreviations: AD, Alzheimer’s disease; CJD, Creutzfeldt–Jakob disease; fCJD, familial CJD; GSS, Gerstmann–Sträussler–Scheinker syndrome; NA, not available; NOS, not otherwise specified; PSP, progressive supranuclear palsy.