Subtypes of LS cause different manifestations of disease involvement and damage; a) pansclerotic morphea, affecting all four extremities and some of trunk b) linear scleroderma of the head, ‘en coup de sabre’, resulting in a deep linear band down the mid forehead with skull depression, c) linear scleroderma extremity, causing elbow, wrist and significant finger joint contracture, d) linear scleroderma of the head, hemifacial atrophy/Parry Romberg, atrophy of left face with associated brainstem lesion.