Defects in Intrinsec and Innate Immunity. AD Autosomal Dominant inheritance, AR Autosomal Recessive inheritance, BCG Bacilli Calmette-Guérin, BL B lymphocyte, CMC Chronic mucocutaneous candidiasis, HSV Herpes simplex virus, IFNγ Interferon gamma, Ig Immunoglobulin, IL interleukin, LOF Loss-of-function, MSMD Mendelian Susceptibility to Mycobacterial Disease, PMN Neutrophils, XL X-Linked inheritance