Figure 1.

ECG: electrocardiogram; PFT: pulmonary function testing; Dlco: diffusion capacity of the lung for carbon monoxide; BGA: blood gas analysis; HRCT: high-resolution computed tomography; RV: right ventricle; V/Q: ventilation/perfusion; CTEPH: chronic thromboembolic pulmonary hypertension; RHC: right heart catheter; PA: pulmonary angiography; PEA: pulmonary endarterectomy; mPAP: mean pulmonary artery pressure; PAWP: pulmonary arterial wedge pressure; CTD: connective tissue disease; CHD: congenital heart disease; PVOD: pulmonary veno-occlusive disease; PCH: pulmonary capillary haemangiomatosis. Reproduced from [3] with permission from the publisher.