Table 1.

Patient characteristics

				Grip strength
Table	Deletion/	Age at	Age at onset of	Right	Left	Creatinekinase	Frequency wheelchair/ scooter
ID	mutation	study	symptoms	arm	arm	(U L–1)	use	Medications
1	3–7	21	6	8	9	2522	Frequently	Chromium, creatine, enalapril
2	3–7	24	12	34	33	3863	Rarely	None
3	45–47	18	12	29	35	1510	Never	None
4	45–47	40	4	14	18	1473	Frequently	Lisinopril, simvastatin
5	45–48	44	31	25	32	616	Rarely	None
6	45–48	41	35	40	43	657	Never	None
7	45–48	44	30	39	41	455	Never	None
8	14–44	51	47	20	18	917	Never	None
9	Splice donor Ex46	13	25	44	46	3574	Never	CoQ10, protein supplement, royal jelly
10	Splice donor Ex25	51	26	22	22	444	Rarely	Dermasil
11	Nonsense Mutation Ex29	24	4	32	40	651	Never	Lisinopril, CoQ10, multivitamin
12	48–55	43	38	46	43	554	Never	Prednisone
13	Splice Donor Ex46	21	12	39	41	5104	Never	None
14	45–55	40	30	23	20	1552	Never	None
15	45–53	35	7	11	–	2282	Never	None
16	Splice Acceptor Ex26	25	18	17	15	2766	Never	Detrol

Normal creatinine kinase range: 0–171 U L^–1.