Table 3.

Comparison with other chromosome 9 linked FTD/ALS families

Chromosome 9 linked family	Number of families	Number of cases	TDP-43 positive pathology	AAOa (years)		Disease duration (years)		FTD + ALS (%)	FTD or dementia (%)	ALS (%)
				Mean	Range	Mean	Range
Morita [16]	1	14	Yes	55.3	(45–64)	4.3	(1–9)	0	64	36
Vance [18]	1	12	Yes	60.3	(39–72)	3.0	(1–8)	25	17	58
Valdmanis [17]	2	16	NKb	55.1	(45–63)	3.6	(2–9)	19	19	63
Luty [13]	1	11	Yes	52.9	(43–68)	8.6	(1–18)	18	64	18
LeBer [12]	6	31	Yes	57.9	(40–84)	3.6	(1–8)	39	32	29
Gijselinck [15]	1	9	Yes	58.1	(51–65)	6.4	(1–17)	0	89	11
Boxer [14]	1	10	Yes	45.7	(35–57)	5.8	(3–10)	30	50	20
All previous	13	103		55.7	(35–84)	4.6	(1–18)	22	43	35
Gwent kindred	1	9	Yes	42.2	(31–52)	3.6	(1–13)	67	0	33

^aAge at onset

^bNot known