. Author manuscript; available in PMC: 2015 Dec 30.

Published in final edited form as: Haemophilia. 2015 Jul 14;21(5):e384–e388. doi: 10.1111/hae.12747

Table 1.

Phase 1 Demographic Data, Laboratory Values and Bleeding Scores

	Control (n=38)	Affected (n=20)	p value
Male gender (%)	18 (47)	2 (10)	0.006
Mean age years (range)	39 (18 – 72)	36 (18 – 59)	0.294
Mean VWF:Ag IU/mL (range)	1.01 (0.65 – 1.46)^*	0.59 (0.47 – 0.93)	<0.001
Mean VWF:RCo IU/mL (range)	0.69 (0.61 – 1.22)^*	0.38 (0.21 – 0.58)	< 0.001
Mean FVIII IU/mL (range)	1.34 (0.71 – 1.49)^*	0.71 (0.47 – 0.93)	< 0.001
Blood Group O (%)	15 (40)	16 (80)	0.001
Mean Self-BAT BS (range)	1.2 (0 – 4)	10 (4 – 17)	< 0.001
Mean ISTH-BAT BS (range)	1.5 (0 – 4)	11 (5 – 20)	< 0.001

VWF:Ag = VWF antigen, VWF:RCo = VWF ristocetin cofactor activity, FVIII = Factor VIII, Chi-square analysis was performed for categorical variables, and Mann-Whitney for continuous variables.

Data from 2 control subjects were excluded due to sample thaw prior to analysis.