Fig. 5. Neurotologic findings in the index case (patient 1). A: Bithermal caloric tests show a left-side caloric paresis of 74%. B: Pure-tone audiometry shows complete hearing loss on the left side. No cervical (C) or ocular (D) vestibular-evoked myogenic potentials can be evoked when stimulating the left ear. MRI reveals a large tumor (3.4×3.2 cm) involving the left cerebellopontine angle (E). F: Performing HITs using a magnetic search coil technique show decreased gains for all six semicircular canals. AC: anterior semicircular canal, HC: horizontal semicircular canal, PC: right posterior semicircular canal.