Skip to main content
. Author manuscript; available in PMC: 2017 Jan 1.
Published in final edited form as: J Inherit Metab Dis. 2015 Aug 11;39(1):17–24. doi: 10.1007/s10545-015-9882-0

Table.

Caloric and macronutrient composition of dietary interventions modeled during acute metabolic decompensation due to dietary nonadherence or infection/anorexia. S1 – Step 1, S2 – Step 2, S3 – Step 3.

Condition kcal protein fat carbohydrate
%kcal g/kg %kcal g(g/kg/d) % kcal g (mg/kg/min)
Prior to acute metabolic decompensation

Baseline 2580 10 0.8 30 86 60 387

Acute metabolic decompensation

Overeating (2 days) 3080 15 1.4 30 102 55 423
Infection/anorexia (2 days) 1290 10 0.4 30 43 60 194

Reintroduction of oral calories following acute metabolic decompensation

50% Diet (SI) 1290 10 0.4 30 43 60 193
75% Diet S2 1934 10 0.6 30 64 60 290
100% Diet (S3) 2578 10 0.8 30 86 60 387

Parenteral nutrition scenarios

DEX 2800 100 824 (7)
HYPO 1400 100 412 (3.6)
ISO 2800 50 140 (1.75) 50 412 (3.6)