Table 1.
Clinical Features and Follow-up Data
| Case no. | Diagnosis (RMS) | Age/sex | site | Size (cm × cm × cm) | Presentation | Treatment | Gradea | Stageb | Follow-up (mo) |
|---|---|---|---|---|---|---|---|---|---|
| 1 | Spindle cell | 42 y/M | Left upper arm | 5.2×3.2×2.5 | Painless solid mass with poor mobility and related demarcation | Surgery and chemotherapy | 3 | III | DOD (24) |
| 2 | Spindle cell | 30 y/M | Left lower quadrant of abdomen wall | 14.0×9.8×9.0 | Painless and cystic-solid mass with demarcation and peritoneum involved focally | Surgery | 3 | III | In situ Rec (10) |
| 3 | Spindle cell | 49 y/M | Next to left glottis in larynx | 2.4×1.8×1.5 | Hoarseness; solid mass with focal calcification and cervical lymphadenopathy | Surgery and radiotherapy | 1 | I B | AWOD (5) |
| 4 | Spindle cell | 5 mo/F | Left orbit | 2.8×2.7×0.6 | Left eye swelling, expanded palpebral fissure and protopsis | Surgery | 2 | II A | AWD (5) |
| 5 | Spindle cell | 28 y/M | nasopharynx | 5.0×5.0×1.0 | Nasal obstruction, rhinorrhoe and occasional headache; solid mass involved sphenoid sinus | Surgery | 3 | III | AWD (1) |
| 6 | Spindle cell | 52/M | Left thigh | 21×9.0×8.5 | Solid mass with heavy tenderness; mobility limitation | Surgery | 2 | IV | In situ Rec and metastasis to stomach (12) |
| 7 | sclerosing | 24/F | Back of right hand | 3.4×2.5×1.5 | Solid and demarcated mass gradually increase during 10 years and repeatedly recurred | Surgery | 1 | I A | NED (1) |
| 8 | sclerosing | 18/M | Right groin | 16.5×9.0×9.0 | Painless solid mass with compressed peripheral vessels | Surgery and chemotherapy | 1 | I B | AWOD (6) |
| 9 | sclerosing | 36/F | Left pars buccalis | 4.8×3.5×2 | Solid increasing mass with ulcer formation and pain feelings | Surgery | 1 | I A | AWOD (8) |
| 10 | sclerosing | 57/F | Right parotid gland | 2.3×1.8×1.5 | Solid painless mass with mouth-opening limitation | Surgery | 1 | I A | AWOD (13) |
a
using FNCLCC grading system;
b
sing AJCC anatomic staging system;
AWD, alive with diseases; AWOD, alive without evidence of disease; DOD, die of disease; mo, months; NA, not available; NED, no evidence of disease; Rec, recurrence.