Table 1. Summary of the neoplasms reported.
| Overall | IC2-LoM | UPD | IC1-GoM | P-value | |||||
|---|---|---|---|---|---|---|---|---|---|
| n | % | n | % | n | % | n | % | ||
| Malignant tumors | 25a | 7.5% | 4 | 2.1% | 13 | 14.9% | 8 | 25.8 | <0.001 |
| Wilms' tumor | 10 | 3.1% | − | − | 3 | 3.4% | 7 | 22.6% | <0.001 |
| Hepatoblastoma | 5 | 1.6% | − | − | 5 | 5.7% | − | − | 0.003 |
| Neuroblastoma | 4 | 1.3% | 2 | 1.1% | 2 | 2.3% | − | − | |
| Pancreatoblastoma | 2 | 0.6% | − | − | 1 | 1.1% | 1 | 3.2% | |
| Adrenal carcinoma | 1 | 0.3% | − | − | 1 | 1.1% | − | − | |
| Rhabdomyosarcoma | 1 | 0.3% | 1 | 0.5% | − | − | − | − | |
| Hemangiotelioma | 1 | 0.3% | − | − | 1 | 1.1% | − | − | |
| Germinoma | 1 | 0.3% | 1 | 0.5% | − | − | − | − | |
| Benign tumors | 14 | 4.4% | 4 | 2.1% | 6 | 6.9% | 4 | 12.9% | 0.009 |
| Hepatic angioma | 9 | 2.8% | 4 | 2.1% | 4 | 4.6% | 1 | 3.2% | |
| Thyroid adenoma | 1 | 0.3% | − | − | 1 | 1.1% | − | − | |
| Mammary gland fibroma | 1 | 0.3% | − | − | 1 | 1.1% | − | − | |
| Lipoma | 1 | 0.3% | − | − | − | − | 1 | 3.2% | |
| Pilomatrixoma | 1 | 0.3% | − | − | − | − | 1 | 3.2% | |
| Cavernous hemangioma | 1 | 0.3% | − | − | − | − | 1 | 3.2% | |
a
Twenty-three patients: one patient with UPD developed a pancreatoblastoma and a neuroblastoma.