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. Author manuscript; available in PMC: 2016 Jan 25.
Published in final edited form as: Lymphology. 2009 Jun;42(2):66–76.

TABLE 2.

Clinical Phenotypes and Associated Lymphatic Findings

Clinical Presentation* Lymphatic Abnormalities
Cancer and tumor metastasis Lymphatic invasion
Conjunctival myxoma Lymphatic dilation
Conjunctival Lymphangiectasia Lymphatic dilation
Chemosis Lymphatic defects or blockade
Mustard gas keratitis Conjunctival lymphatic dilation
Corneal inflammation Lymphangiogenesis
Transplant rejection Lymphatic drainage
Orbital cellulitis Impaired lymphatic drainage
Pilomatricoma Lymphatic dilation
Chalazion Flattened lymphatics
Dermatochalasis Lymphatic dilation
Blepharochalasis Lymphatic proliferation and dilation
Avian myopia Lymphatic distension
Harlequin and Horner syndromes Lymphatic surgery complication
Hyperthyroidism/Myxedema Lymphatic dilation
Lymphatic filariasis Lymphatic dissemination
Toxoplasmosis Lymphatic dissemination
Tuberculosis Lymphatic dissemination
Trichinosis Lymphatic dissemination
Conjunctival kaposi’s sarcoma Lymphovascular neoplasm
Meige syndrome/Conjunctival edema Lymphatic structural defects
Milroy’s disease/Eyelid and conjunctival edema Lymphedema
Lymphedema-ptosis syndrome Lymphedema
Lymphedema-distichiasis syndrome Lymphatic hyperplasia
Lymphedema-hypoparathyroidism syndrome Lymphedema
Mucke syndrome/Conjunctival edema Lymphedema
Chorioretinal dysplasia-lymphedema syndrome Lymphedema
Melkersson-Rosenthal syndrome/Eyelid edema Lymphatic dilatation
Lymphedematous rosacea/Eyelid edema Impaired lymphatic drainage
Turner’s syndrome/Conjunctival chemosis Lymphangiectasis
Noonan syndrome/Ptosis and hypertelorism Intestinal lymphangiectasia
Persistent müllerian derivatives Intestinal lymphangiectasia
Behcet’s disease Intestinal lymphangiectasia
Venous-lymphatic malformations/Lymphangiomas Lymphatic malformation
*

Local forms or systemic diseases with ocular manifestations.