Table 1. Clinical features of 17 patients identified to have recurrent fever and multi-system inflammation without infectious or autoimmune evidence.
| Patient | Sex | Age | Clinical symptoms or signs except fever | ||||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| OU/GU | Arthritis | Macular rash | Sore throat | Myalgia | HA | LAP | Sacroiliitis | EN | Abd pain & diarrhea | HSM | Serositis | Others | |||
| 1 | F | 19 | +/- | + | + | + | + | ||||||||
| 2 | M | 18 | Monophasic, hip | + | +/C | +* | Gluteal myositis & sterile abscess | ||||||||
| 3 | F | 38 | +/+ | +/C | |||||||||||
| 4 | M | 37 | +/U | + | + | + | + | + | Hepatitis, encephalitis | ||||||
| 5 | F | 55 | +/P | + | + | + | |||||||||
| 6 | M | 50 | +/- | DVT, encephalitis | |||||||||||
| 7 | M | 37 | Cyclic, PL | + | + | + | |||||||||
| 8 | F | 47 | +/+ | Cyclic, OG | + | + | + | + | Found to have BD | ||||||
| 9 | F | 37 | +/+ | + | + | +/C | |||||||||
| 10 | M | 37 | + | + | + | + | |||||||||
| 11 | F | 28 | +/- | +/C | + | ||||||||||
| 12 | F | 22 | +/- | Monophasic, PL | + | + | + | + | |||||||
| 13 | F | 40 | +/- | Cyclic, OG | + | + | + | +* | |||||||
| 14 | F | 37 | +/+ | Cyclic, OG | + | ||||||||||
| 15 | M | 43 | Cyclic, PL | ||||||||||||
| 16 | M | 22 | +/- | Cyclic, OG | + | ||||||||||
| 17 | F | 53 | + | +* | Gluteal myositis & sterile abscess | ||||||||||
| Total frequency | 10/4 | 8 | 7/2 | 7 | 7 | 6 | 5/4 | 3 | 3 | 3 | 3 | 2 | |||
*No chronic inflammatory back pain during the course of illness; sacroiliitis confirmed in magnetic resonance imaging. Abd, abdominal; BD, Behcet's disease; C, cervical lymphadenopathy; DVT, deep vein thrombosis; EN, erythema nodosum-like lesions; F, female; GU, genital ulcers; HA, non-organic headache; HSM, hepatosplenomegaly; LAP, lymphadenopathy; M, male; OG, oligoarthritis; OU, oral ulcers; P, pruritic; U, Urticarial; PL, polyarthritis.