Table 2.
The classification of clinical severity score, mean age and EcoRI fragment in 173 facioscapulohumeral muscular dystrophy patients
Groups* | Male | Female | ||||||
---|---|---|---|---|---|---|---|---|
n | Age (years)† | EcoRI fragment (kb) | Range (kb) | n | Age (years)† | EcoRI fragment (kb) | Range (kb) | |
I | 3 | 40.0 ± 12.5 | 19.3 ± 3.8 | 15–22 | 16 | 35.2 ± 10.2 | 19.7 ± 5.8 | 13–30 |
II | 22 | 28.2 ± 10.1 | 21.7 ± 6.1 | 12–35 | 14 | 29.7 ± 12.0 | 20.1 ± 4.5 | 10–28 |
III | 18 | 25.9 ± 5.9 | 20.0 ± 5.6 | 13–30 | 9 | 30.0 ± 13.4 | 19.3 ± 4.1 | 13–24 |
IV | 27 | 30.0 ± 10.7 | 19.2 ± 4.4 | 12–26 | 20 | 30.3 ± 12.1 | 21.2 ± 5.2 | 13–30 |
V | 15 | 34.3 ± 13.5 | 18.6 ± 3.9 | 13–29 | 13 | 36.3 ± 13.2 | 16.5 ± 5.8 | 10–27 |
VI | 4 | 28.5 ± 7.6 | 13.5 ± 2.7 | 10–15 | 12 | 33.4 ± 11.1 | 18.6 ± 4.3 | 14–27 |
Total | 89 | 29.7 ± 10.5 | 19.6 ± 5.2 | 10–35 | 84 | 32.2 ± 11.9 | 19.4 ± 5.2 | 10–30 |
*Groups according to clinical severity score. I: Asymptomatic individuals; II: 1.5; III: 2–2.5; IV: 3; V: 3.5; VI: 4–5; †Age: The age on examination.