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. 2016 Feb 5;4:9. doi: 10.1186/s40478-016-0276-9

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© Sandell et al. 2016

Open AccessThis article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made. The Creative Commons Public Domain Dedication waiver (http://creativecommons.org/publicdomain/zero/1.0/) applies to the data made available in this article, unless otherwise stated.

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Fig. 3 — a, c, d. Vastus lateralis muscle of a 72-year-old female (FF1, III-12): moderate or strong expression of proteins myotilin (a), desmin (c) and alphaB-crystallin (d) in the myofibrillar lesions with aggregates on immunohistochemistry. b. Congo red staining viewed through Texas-red filters shows numerous congophilic fluorescent deposits in muscle fibers. e. Dystrophin-2 showed ectopic expression of mild or moderate intensity in the same regions. f, g, h. The protein accumulations showing CASA complex proteins BAG3 (f), HSPB8 (g), and DNAJB6 (h)