Table 2.
Antibodies used in immunohostochemical stainings, their dilutions and supplier
| Antibody | Dilution | Supplier |
|---|---|---|
| Myotilin | 1:50 | Leica Biosystems, Novocastra |
| Alpha B crystallin | 1:10 | Leica Biosystems, Novocastra |
| Desmin | 1:800 | Biogenex |
| Dystrophin 2 (c-terminus) | 1:100 | Leica Biosystems, Novocastra |
| SMI-31 | 1:1000 | Biosite |
| SMI-310 | 1:400 | Abcam |
| TDP-43 | 1:175 | Proteintech Europe |
| P62 (SQSTM1) | 1:100 | Santa Cruz Biotechnology |
| Ubiquitin | 1:300 | Dako |
| LAMP2 | 1:50 | Southern Biotech |
| LC3 | 1:50 | Novus Biologicals |
| LC3B | 1:50 | Cell Signaling technology |
| VCP | 1:600 | Thermo Scientific |
| FHL-1 | 1:200 | Lifespan biosciences |
| DNAJB6 | 1:100 | Abnova |
| HSPB8 | 1:200 | Abcam |
| BAG3 | 1:800 | Proteintech Europe |
| Proteasome | 1:30 | Atlas antibodies |
| Beta-amyloid | 1:30 | Leica Biosystems, Novocastra Life |
| Amyloid precursor protein | 1:50 | Biosciences |
| Wip1 | 1:50 | Sigma |
| Dystrophin 1 (rod domain) | 1:40 | Leica Biosystems, Novocastra |
| Dystrophin 2 (c-terminus) | 1:100 | Leica Biosystems, Novocastra |
| Dystrophin 3 (N-terminus) | 1:20 | Leica Biosystems, Novocastra |
| Dysferlin | 1:200 | Leica Biosystems, Novocastra |
| α-Sarcoglycan | 1:100 | Leica Biosystems, Novocastra |
| β-Sarcoglycan | 1:100 | Leica Biosystems, Novocastra |
| γ-Sarcoglycan | 1:15 | Leica Biosystems, Novocastra |
| α-Dystroglycan | 1:200 | Millipore, Upstate |
| Caveolin 3 | 1:150 | Santa Cruz Biotechnology |
| Merosin Laminin Alpha 2 Chain | 1:500 | USBiological |
| Utrophin | 1:20 | Leica Biosystems, Novocastra |
| Spectrin | 1:50 | Leica Biosystems, Novocastra |