. Author manuscript; available in PMC: 2016 Feb 6.

Published in final edited form as: Ann Neurol. 2003 Mar;53(3):354–365. doi: 10.1002/ana.10466

Table 1.

Null Kindreds with Affected Male Subjects

			Motor Conduction Velocities
			Ulnar Nerve				Median Nerve				Peroneal Nerve
Subject	Age (yr)	Side	DML (ms)	Vel (m/s)	Amp (mV)	F (ms)	DML (ms)	Vel (m/s)	Amp (mV)	F (ms)	DML (ms)	Vel (m/s)	Amp (mV)	F (ms)
DelG1 family
VI-7	17	R
		L	*4.0*	*36.0*	7.0	*42.8*	*5.0*		5.1		*9.5*	*29.0*	*0.9*
VI-17	18	R	*3.9*	*30.0*	5.5	*48.4*	*6.1*	*38.0*	*3.0*		*10.0*	*27.0*	3.2
		L	*6.2*	*31.0*	9.1	*52.0*	*8.1*	*25.0*	*0.7*		*10.3*	*20.0*	*0.3*
VI-6	20	R	3.3	*47.0*	8.8	*34.6*	*5.4*	*44.0*	6.9	*36.6*	*7.0*	*24.0*	2.7	*66.2*
V-5	39						*7.0*	*42.0*			*6.9*	*28.0*	*0.6*
V-29	36						*5.2*					*38.0*
VI-13	16	L	*4.5*	*38.0*	6.5	*38.6*	*5.7*	*37.0*	5.1	*35.4*	5.4	*27.0*	6.3
M1T
Family 1	4	R	*4.6*	*45.0*	*2.5*	*34.2*	4.4	57.0		29.6	*6.9*	*23.0*	*0.7*
Family 2	14	R					*5.8*	36			4.8	33
Same patient, age 20 yr	20	R					4.2	42			*9.8*	33
PLP1 Del family							*6.5*	41			*11.1*	34
1-1	40	R	*3.9*	40	*1.7*	30.5	*6.4*	30	10.1
Normal values			<3.5	>50	>6.0	<33	<4.5	>48	>4.0	<32	<6.0	*>41*	>2.0	<56

			Sensory Conduction Velocities
			Ulnar Nerve		Median Nerve		Sural Nerve
Subject	Age (yr)	Side	Vel (m/s)	Amp (μV)	Vel (m/s)	Amp (μV)	Vel (m/s)	Amp (μV)
DelG1 family
VI-7	17	R	*43.0*	*11.0*	*42.0*	*15.9*
		L	*38.0*	*11.6*	*38.0*	*4.3*	*33.0*	6.1
VI-17	18	R					38.0	*5.1*
		L			*27.0*	*8.3*
VI-5	20	R			*48.0*	30.0
V-29	36	L			*40.0*	*4.9*
VI-13	16	L	*47.0*	*14.4*	60.0	31.1	42.0	9.0
Normal values			>54	>20	>50	>20	>35	>6.0

Abnormal values are in boldface, italic type.

DML = distal motor latency; Vel = nerve conduction velocity; Amp = compound action motor potential; F = F-wave latency.