Table 1.
Recent epidemiologic study results on moyamoya disease
| Authors/Published year | Country | Year of survey | Research method | No. of patients | Sex ratio (female/male) | Age distribution | Prevalence (per 100,000) | Incidence (per 100,000) |
|---|---|---|---|---|---|---|---|---|
| Wakai et al. 1997 | Japan | 1995 | Hospital survey | 1,176 | 1.8 | Two peaks | 3.16 | 0.35 |
| 1st 10-14 in both sexes | ||||||||
| 2nd 45-49 in men | ||||||||
| 40-45 in women | ||||||||
| Kuriyama et al. 2008 | Japan | 2004 | Hospital survey | 1,240 | 1.8 | Three peaks | 6.03 | 0.54 |
| 1st 10-14 in men | ||||||||
| 20-24 in women | ||||||||
| 2nd 35-39 in men | ||||||||
| 50-54 in women | ||||||||
| 3rd 55-59 in men | ||||||||
| Baba et al. 2008 | Hokkaido, Japan | 2002-2006 | Survey based on registered Intractable diseases of the Ministry of Health, Labour, Welfare | 267 | 1:2.2 | 1st 5-9 | 10.5 | 0.94 |
| 2nd 45-49 | ||||||||
| Miao et al. 2010 | Nanging, China | 2000-2007 | Hospital survey and chart review | 202 | 1.1 | Two peaks | 3.92 | |
| 1st 5-9 | ||||||||
| 2nd 35-39 | ||||||||
| Yim et al. 2012 | Korea | 2004-2008 | National Health Insurance | 2,987 (year 2005) | 1.94 | Two peaks | 6.3 | |
| 3,429 (year 2006) | 1st 10-19 | 7 | ||||||
| 4,051 (year 2007) | 2nd 40-49 | 8.6 | ||||||
| 4,517 (year 2008) | 9.1 | 1 (year 2008) | ||||||
| Ahn et al. 2014 | Korea | 2007-2011 | Registration program for rare intractable diseases under National Health Insurance | 4,047 (year 2007) | 1.9 | Two peaks | 8.2 | 1.7 |
| 4,975 (year 2008) | Incidence | 10 | 1.9 | |||||
| 6,038 (year 2009) | 1st 5-14 | 12.1 | 2.2 | |||||
| 7,031 (year 2010) | 2nd 45-54 | 13.9 | 2.1 | |||||
| 8,154 (year 2011) | Prevalence | 16.1 | 2.3 | |||||
| Chen et al. 2014 | Taiwan | 2000-2011 | Taiwan National Health Insurance | 422 | 1.4 (overall) | two peaks (incidence) | 1.61 (yr 2011) | 0.14 (year 2000-2001) |
| 1.1 (2000-2005) | 1st 5-9 in men | 0.12 (year 2002-2003) | ||||||
| 1.7 (2006-2011) | 10-14 in women | 0.12 (year 2004-2005) | ||||||
| 2nd 40-44 in both | 0.15 (year 2006-2007) | |||||||
| 0.17 (year 2008-2009) | ||||||||
| 0.20 (year 2010-2011) | ||||||||
| Uchino et al. 2005 | Washington state and California | 1987-1998 (Washington) | Hospital record | 298 | 2.2 | Two peaks | 0.086 (overall) | |
| 1991-1998 (California) | 1st 5-9 | 0.28 (Asian American) | ||||||
| 2nd 55-59 | 0.13 (African American) | |||||||
| 0.06 (White) | ||||||||
| 0.03 (Hispanic) |