Table 3.
Clinical features of MIC patients
| Gender |
AD |
Cause of death |
Electrocardiogram |
Echocardiogram |
Medication |
||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Rhythm | LVH | Strain | Other | EF% | LVEDD | LVESD | LVWT VS | LVWT PW | |||||
| H MIC | |||||||||||||
| 1 | M | 35 | SD | Sinus | Yes | Yes | RVH | N | N | N | 16 | 15 | BB, ACEi |
| 2 | M | 45 | SD | Sinus | Yes | Yes | No | 45 | N | N | N1 | N1 | ACEi |
| 3 | M | 36 | SD | Sinus LBBB | Yes | No | Short PR | 55 | 44.5 | 34.5 | 12.5 | 9.5 | BB, ACEi |
| FH MIC | |||||||||||||
| 4 | M | 30 | CHF2 | Sinus, biventricular PM | No | No | No | 15 | 62 | 59 | N1 | N1 | Dobutamine |
| 5 | M | 233 | CHF | Sinus | Yes | Yes | TWI | 17 | 82 | 72 | 25 | 16 | BB, ACEi |
| 6 | M | 203 | CHF | Sinus | Yes | Yes | TWI | 25 | 69 | 63 | 21 | 18 | BB, ACEi |
AD: age at death.
LVH: left ventricle hypertrophy.
LVEDD: left ventricular end-diastolic diameter.
LVESD: left ventricular end-systolic diameter.
LVWT: left ventricular wall thickness.
PW: posterior wall.
SD: sudden death.
RVH: right ventricle hypertrophy.
BB: beta blockers.
ACEis: ACE inhibitors.
LBBB: left bundle brank block.
PR: PR interval.
CHF: congestive heart failure.
PM: pace maker.
TWI: T-wave inversion.
N: normal.
Upper limit of normal.
Sudden death while waiting for cardiac transplant.
Cardiac transplant.