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. 2016 Jan 12;127(7):820–828. doi: 10.1182/blood-2015-08-618561

Table 1.

Classification of pulmonary hypertension according to the World Symposium on Pulmonary Hypertension

Group Definition
1 Pulmonary arterial hypertension
2 Pulmonary hypertension due to left heart disease
3 Pulmonary hypertension due to lung diseases and/or hypoxia
4 CTEPH
5 Pulmonary hypertension with unclear or multifactorial mechanisms