Table 1.

Selected reports of primary immunodeficiency diseases in the patients with BCG complications.

Study	Year	Country/Origin	No. of patients with BCG complications	No. of Patients with PIDs	No. of SCID patients	No. of CGD patients	No. of MSMD patients	No. of other PIDs patients	Ref.
Toida & Nakata	2007	Japan	39 (review)	19(48.7%)	4	5	4 IFN-γR1 deficiency	6 cell-mediated immune defects	68
Li et al	2010	China	18	12(66.7%)	3	7	2 IL-12/IFN-γ pathway deficiency	–	69
Lee et al	2009	Taiwan	18	18(100%)	12	2	3 IFN-γR1 deficiency	1 chronic mucocutaneous candidiasis	70
Afshar Paiman et al	2006	Iran	17	10(58.8%)	8	1	–	1 cell-mediated immune defects	40
Sadeghi-Shabestari et al	2009	Iran	11	11(100%)	7	1	1 IL12R deficiency 2 Other MSMD	–	71
Scoazec et al	1984	France	11	11(100%)	5	3	–	1 Di George’s syndrome, 3 unclassified conditions	72
Gonzalez et al	1989	Chile	9	9(100%)	2	3	–	4 cell-mediated immune defects	73
Lee et al	2009	Taiwan	8	4(50%)	2	–	–	1 primary autoimmune neutropenia, 1 chronic mucocutaneous candidiasis	74
Jacob et al	1996	Brazil	4	4(100%)	1	1	–	1 cell-mediated immune defects, 1 chemotaxis defect	75
Abramowsky et al	1993	Chile-USA	4	4(100%)	2	–	–	2 cell-mediated immune defects	76
Romanus et al	1993	Sweden	4	3(75%)	–	–	–	–	77
Verma et al	2008	India	3	3(100%)	2	–	–	1 CD8 deficiency	78
Santos et al	2010	Portugal	3	3(100%)	1	–	2 IFN-γR1 deficiency	–	11
Bustamante et al	2007	France	3	3(100%)	–	–	3 Novel XL-MSMD	–	79
Antaya et al	2001	Qatar- Panama	2	2(100%)	1	–	–	1 cell-mediated immune defects	80
Pasic et al	1998	Yugoslavia	1	1(100%)	–	–	–	1 hyper-immunoglobulin E syndrome	62
Talbot et al	1997	Brazil	1	1(100%)	–	–	–	1 cell-mediated immune defects	6
Fischer et al	1980	France	1	1(100%)	–	–	–	1 cell-mediated immune defects	81
Mackay et al	1980	Scotland	1	1(100%)	–	–	–	1 cell-mediated immune defects	82