Table II.
Profile of HHT patients by gene status.
| HHT2 | HHT1 | p | |
|---|---|---|---|
| Number of telangiectases | avg (range) | avg (range) | |
| Face | 2.7 (0-24) | 2.8 (0-56) | 0.9618 |
| Lips | 4.2 (0-36) | 5.7 (0-36) | 0.1561 |
| Mouth | 4.5 (0-30) | 4.9 (0-50) | 0.7459 |
| Hands | 18.8 (0-165) | 13.6 (0-129) | 0.2306 |
| Age of onset for epistaxis | 12.2 (1-48) | 9.4 (1-47) | 0.0047 |
| Age at first intervention | 43.8 | 41.5 | 0.5845 |
| Treatments/Interventions | |||
| Oral iron | 39.0% | 23.9% | 0.0321 |
| Iron infusion | 19.5% | 12.7% | 0.2222 |
| RBC transfusion | 22.8% | 12.7% | 0.0849 |
| Laser or cautery (electric or chemical) | 52.8 | 36.6 | 0.0291 |
| Young's procedure or septal dermoplasty | 10.6 | 7 | 0.4147 |
| ESS range | 3.94 (0-10) | 3.18 (0-9.1) | 0.0434 |
| Mild (1-3) | 50.8% | 52.6% | 0.8162 |
| Moderate (3-7) | 38.3% | 40.4% | 0.7898 |
| Severe (7-10) | 10.9% | 7.0% | 0.4062 |
Abbreviations:
• ESS- epistaxis severity score
• HHT- hereditary hemorrhagic telangiectasia