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. 2016 Feb 21;21:55–58. doi: 10.1016/j.ijscr.2016.02.019

Table I.

The incidence of hepatoblastoma in inherited syndromes.

Syndrome Source Incidence
FAP John Hopkins polyposis registry [4] 847 times the SEER population incidence (95% CI: 230–2168)
BWS BWS registry [5] 2280 times the US population incidence (95% CI: 928–11,656)
Edwards syndrome J. Med. Case reports [6] 7 case reports in very rare disease with poor survival rate beyond the first year of life

(a) FAP: familial adenomatous polyposis, (b) BWS: Beckwith–Wiedemann syndrome.