Table 1.
Criteria | Sub-criteria | Score |
---|---|---|
Skin thickening of fingers of both hands extending proximal to the metacarpolphalangeal (MCP) joints | 9 | |
Skin thickening of fingers only (only count higher score) | - Puffy fingers - Sclerodactyly of the fingers (distal to the MCP joints but proximal to the proximal interphalangeal (PIP) joints |
2 4 |
Fingertip lesions (only count higher score) | - Digital tip ulcers - Fingertip pitting scars |
2 3 |
Telangectasia | 2 | |
Abnormal nailfold capillaries | 2 | |
Lung involvement (maximum score of 2) | - PAH - ILD |
2 2 |
RP | 3 | |
SSc-associated autoantibodies (anti-centromere, anti-topoisomerase I (anti-Scl-70), anti-RNA polymerase III) | 3 |
The total score is calculated by adding the highest score in each category. Those with a score of at least 9 are classified as having SSc.
Modified from [6].